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Adrenocorticotropic Hormone-Secreting Esthesioneuroblastoma with Ectopic Cushing's Syndrome

Yonsei Medical Journal 2020년 61권 3호 p.257 ~ 261
 ( Chung Young-Soo ) - Yonsei University College of Medicine Department of Neurosurgery

나민균 ( Na Min-Kyun ) - Yonsei University College of Medicine Department of Neurosurgery
구철룡 ( Ku Cheol-Ryong ) - Yonsei University College of Medicine Department of Internal Medicine
김세훈 ( Kim Se-Hoon ) - Yonsei University College of Medicine Department of Pathology
김의현 ( Kim Eui-Hyun ) - Yonsei University College of Medicine Department of Neurosurgery

Abstract


Esthesioneuroblastoma as a source of ectopic Cushing's syndrome is rare, and to the best of our knowledge, only 20 cases have been reported worldwide. A 46-year-old healthy man visited a local clinic for general weakness and hyposmia, and underwent examination with serial endocrinological workup and brain imaging. 68Gallium-DOTA-TOC positron emission tomography scan was helpful where diagnosis of sellar MRI and inferior petrosal sinus sampling were discordant. Combined transcranial and endoscopic endonasal approach surgery was performed, and a diagnosis of esthesioneuroblastoma was given.

키워드

Cushing's disease; ectopic ACTH syndrome, esthesioneuroblastoma; positron emission tomography
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