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A Case of Crohn¡¯s Disease Associated with Turner Syndrome
Á¶¿ëÀº ( Cho Yong-Eun ) - µ¿±¹´ëÇб³ Àǰú´ëÇÐ °æÁÖº´¿ø ³»°úÇб³½Ç
¾çâÇå ( Yang Chang-Heon ) - µ¿±¹´ëÇб³ Àǰú´ëÇÐ ³»°úÇб³½Ç
ÀÌÁßÇö ( Lee Joong-Hyun ) - µ¿±¹´ëÇб³ °æÁÖº´¿ø ³»°ú
¹ÚÁ¤¹è ( Park Jeong-Bae ) - µ¿±¹´ëÇб³ Àǰú´ëÇÐ ³»°úÇб³½Ç
±èÀçÇÐ ( Kim Jae-Hak ) - µ¿±¹´ëÇб³ Àǰú´ëÇÐ ³»°úÇб³½Ç
ÀÓÀ±Á¤ ( Lim Yun-Jeong ) - µ¿±¹´ëÇб³ Àǰú´ëÇÐ Àϻ꺴¿ø ³»°úÇб³½Ç
Abstract
32¼¼ÀÇ ÅͳÊÁõÈıº ȯÀÚ°¡ 10´ë ¸»ºÎÅÍ ½ÃÀÛµÈ ¹Ýº¹µÇ´Â ÇϺ¹ºÎ ÅëÁõ°ú ¼³»ç°¡ 1´Þ ÀüºÎÅÍ ¾ÇÈµÇ¾î ³»¿øÇÏ¿´´Ù. ´ëÀå³»½Ã°æ ¼Ò°ß¿¡¼ Ç×¹®¿¬ »ó¹æ 50 cm±îÁö Á÷Àå°ú »óÇà°áÀå¿¡ Á¾ÁÖ ±Ë¾ç°ú Áöµµ»ó ȤÀº µÕ±Ù ¸ð¾çÀÇ ¾ÆÇÁŸ ±Ë¾çÀÌ °üÂûµÇ¾ú°í, ±¸ºÒ°áÀå¿¡¼´Â Á¶¾àµ¹ Á¡¸· ¼Ò°ß°ú ÇùÂø ¼Ò°ßÀ» º¸¿´´Ù. ´ëÀåÁ¶¿µ¼ú¿¡¼ Àü ´ëÀå¿¡ °ÉÃļ ´Ù¹ß¼º ¹Ì¼¼ °ú¸³»ó°ú ¿øÇüÀÇ Ãæ¸¸°á¼Õ ¼Ò°ßÀ» º¸¿´°í, ÇÏÇà°áÀå°ú ±ÙÁ¢ ±¸ºÒ°áÀå¿¡ Àü¹ÝÀûÀÎ ÇùÂø¼Ò°ßÀ» º¸¿´À¸¸ç, ´ëÀå³»½Ã°æ Á¶Á÷°Ë»ç °á°ú ±Ë¾ç°ú ¸¸¼º ¿°Áõ¼Ò°ßÀ» º¸¿´´Ù. Á¶Á÷¼Ò°ßÀ¸·Î ±Ë¾ç¼º ´ëÀå¿°°ú Å©·Ðº´À» °¨º°Çϱ⠾î·Á¿üÁö¸¸, ÀÓ»óÁõ»ó, ³»½Ã°æ ¼Ò°ß, ´ëÀåÁ¶¿µ¼ú ¼Ò°ßÀ» ¹ÙÅÁÀ¸·Î Å©·Ðº´À¸·Î Áø´ÜÇÏ¿´´Ù. ÅͳÊÁõÈıº ȯÀÚ´Â ¿°Áõ¼º ÀåÁúȯÀÇ ¹ß»ý À§Çèµµ°¡ ÀϹÝÀκ¸´Ù Áõ°¡ÇÏ´Â °ÍÀ¸·Î º¸°í µÈ Àû ÀÖÀ¸³ª, ±¹³»¿¡¼´Â ¾ÆÁ÷ ÅͳÊÁõÈıº ȯÀÚ¿¡¼ Å©·Ðº´ÀÌ µ¿¹ÝµÈ Áõ·Ê º¸°í°¡ ¾ø¾ú´Ù. ÀúÀÚµéÀº 32¼¼ ÅͳÊÁõÈıº ȯÀÚ¿¡¼ Å©·Ðº´À» Áø´ÜÇϰí Ä¡·áÇÑ ¿¹¸¦ °æÇèÇÏ¿© ¹®Çå°íÂû°ú ÇÔ²² º¸°í ÇÑ´Ù.
Turner syndrome is a chromosomal disorder in which of all or part one of the X chromosomes is absent, and this syndrome affects females. The syndrome leads to a constellation of physical findings that often includes congenital lymphedema, a short stature and gonadal dysgenesis. The prevalence of inflammatory bowel diseases in the general population is estimated to be 150¡250 per 100,000 population. A 2-fold increase in the risk of developing inflammatory bowel diseases has been reported in women with Turner syndrome. We describe here a case of Turner syndrome with Crohn¡¯s disease.
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ÅÍ³Ê ÁõÈıº;Å©·Ðº´
Turner syndrome;Crohn¡¯s disease
KMID :
0359020100400040275
DOI :
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