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경부 종괴를 동반한 소아에서의 혈구탐식성 림프조직구증 1례

A Case of Hemophagocytic Lymphohistiocytosis Presenting with Neck Mass in a Child

대한두경부종양학회지 2020년 36권 2호 p.55 ~ 59
길부관, 이동원, 김정규,
소속 상세정보
길부관 ( Kil Bu-Kwan ) - Catholic University of Daegu School of Medicine Department of Otolaryngology-Head and Neck Surgery
이동원 ( Lee Dong-Won ) - Catholic University of Daegu School of Medicine Department of Otolaryngology-Head and Neck Surgery
김정규 ( Kim Jeong-Kyu ) - Catholic University of Daegu School of Medicine Department of Otolaryngology-Head and Neck Surgery

Abstract


Hemophagocytic lymphohistiocytosis (HLH) is a rare but life-threatening one syndrome of excessive immune activation. This immune dysregulation disorder is prominently associated with cytopenias and combinations of clinical signs and extreme inflammation symptoms. For survival, it is important to diagnose early and treat appropriately. We report a case of 10 years old boy who was admitted to the hospital with a month history of fever and cervical lymph node enlargement. There were signs of hemophagocytic histiocytosis in the lymph node and bone marrow. The etiology, diagnosis, and treatment of hemophagocytic lymphohistiocytosis are reviewed.

키워드

Hemophagocytic lymphohistiocytosis; Head and neck neoplasm; Fever; Child; Differential diagnosis

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