잠시만 기다려 주세요. 로딩중입니다.

Amyloid light-chain amyloidosis presented as focal segmental glomerulosclerosis in a kidney transplant recipient

대한이식학회지 2020년 34권 1호 p.66 ~ 70
 ( Park Sung-Hyun ) - Catholic University College of Medicine Seoul St. Mary’s Hospital Department of Internal Medicine

 ( Kwon So-Hyun ) - Catholic University College of Medicine Seoul St. Mary’s Hospital Department of Internal Medicine
이화영 ( Lee Hwa-Young ) - Catholic University College of Medicine Seoul St. Mary’s Hospital Department of Internal Medicine
 ( Lee Su-A ) - Catholic University College of Medicine Seoul St. Mary’s Hospital Department of Internal Medicine
고은정 ( Ko Eun-Jeong ) - Catholic University College of Medicine Seoul St. Mary’s Hospital Department of Internal Medicine
반태현 ( Ban Tae-Hyun ) - Catholic University College of Medicine Seoul St. Mary’s Hospital Department of Internal Medicine
정병하 ( Chung Byung-Ha ) - Catholic University College of Medicine Seoul St. Mary’s Hospital Department of Internal Medicine
최영진 ( Choi Yeong-Jin ) - Catholic University College of Medicine Seoul St. Mary’s Hospital Department of Pathology
양철우 ( Yang Chul-Woo ) - Catholic University College of Medicine Seoul St. Mary’s Hospital Department of Internal Medicine

Abstract


Amyloid light-chain (AL) amyloidosis after kidney transplantation is a rare disease in the world, and only one case of systemic AL amyloidosis after kidney transplantation is reported in Korea. We here report a 46-year-old woman with AL amyloidosis developed after kidney transplantation. The underlying disease of our case was focal segmental glomerulosclerosis (FSGS), and was admitted to hospital for evaluation of proteinuria developed 2 years after kidney transplantation. The patient was initially diagnosed as recurrent FSGS on light microscopy. But, electron microscopic finding was suggestive of amyloidosis and systemic evaluation was consistent with systemic AL amyloidosis. This case provides the importance of differential diagnosis of proteinuria in kidney transplant recipients.

키워드

Amyloid light-chain amyloidosis; Kidney transplantation; Focal segmental glomerulosclerosis
원문 및 링크아웃 정보
 
등재저널 정보