선천성 각막포도종 1예
A Case of Congenital Cornea-fl Staphyloma
이춘식, 박순규, 김광용,
소속 상세정보
이춘식 ( )
부산대학교 의과대학 안과학교실
박순규 ( )
부산대학교 의과대학 안과학교실
김광용 ( )
부산대학교 의과대학 안과학교실
KMID : 0360219770180040391
Abstract
저자들은 4세 남아에서 전형적인 각막포도종을 경험하고 병리조직학적 소견을 관찰하고 중배엽 및 신경외 배엽이 관여한 발육이상으로 생각된 증례를 보고 하였다.
A case of congenital corneal staphyloma was presented. This 4 year-old boy was premature born and received oxygen in theLincubator during one month after birth. He showed mental retardation, articulation disturbance and gait disturbance.
The right eye was free from any anomaly. The left eye was undergone enucleation for cosmetic improvement because of corneal opacity at birth.
A detailed histologic examination of the congenital corneal staphyloma was given; epidermidialization of the corneal epithelium, scarring and vascularization of the stroma, with an absence of Bowman´s membrane were shown. Descemet-endothelial layer was completely defective in keratoiridic and corneal-abnormal pigment layer adhesions, but found in the seperated portion between cornea. and iris.
Iris root was not found in normal position. An abnormal pigment epithelial layer from ciliary epithelium was covered the surface of trabecular meshwork (anterior chamber angle) and an abnormal pigmentation of the trabecular meshwork poorly developed, which was running on iris pigment epithelium and covering inner surface of the cornea.
The ciliary body, especially the process was atrophic. The lens was thin membranous and cataractous. Abnormal fibrinous band in the retinal capillary bed was argyrophilic strand.
It was suggested that these findings of anterior corneal staphyloma was resulted from primary developmental anomaly of mesodermal and/or neuroectodermal tissue.
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