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腫瘍積症을 일으킨 典型的인 Peutz-Jeghers Syndrome

Case Report of Typical Peutz-Jeghers Syndrome Accompanied with Intussusception

대한외과학회지 1962년 4권 5호 p.361 ~ 365
李用雨, 李漢吉,
소속 상세정보
李用雨 (  ) - 가톨릭大學 醫學部 外科學敎室
李漢吉 (  ) - 가톨릭大學 醫學部 外科學敎室

Abstract


Peutz-Jeghers syndrome has a hereditary nature and is characterized by intestinal polyposis associated with characteristic melanin spots. A typical case of Peutz-Jeghers syndrome accompanied with intussusception has been reported and a brief review was made of the literature.
The authors believe this is the first reported case of Peutz-Jeghers syndrome in Korea.
An acutely and chronically ill 21 year old Korean male was admitted with an acute abdomen. This patient had a long-.standing history of repeated intermittent abdominal pain with vomiting. He had small intestinal intussusception which was not. reducible and had to be resected.
On sectioning the specimen, four intestinal polypes were present and one of these was found to be a low grade malignancy. He had typical pigmentation of the lower lip, palms and soles of the feet. His father also had pigmentation of the lip of the same nature since his childhood and died apparently with Peutz-Jeghers syndrome.

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