잠시만 기다려 주세요. 로딩중입니다.

大動脈狹窄, 食道形成不全과 氣管支瘻 및 脊椎骨形成不全을 同伴한 橈骨形成不全症의 1例

Radial dysplasia with juvenile coarctation of the aorta, tracheo-esophageal fistula and multiple hemivertebrae

중앙의학 1967년 13권 3호 p.289 ~ 292
鄭喆永, 李斗鳳, 趙永祺,
소속 상세정보
鄭喆永 (  ) - 가톨릭醫大小兒科
李斗鳳 (  ) - 가톨릭醫大小兒科
趙永祺 (  ) - 가톨릭醫大小兒科

Abstract


This paper reports a 48 hrs. of life, newborn male infant whom had the radial dysplasia with juvenile coarctation of the aorta, tracheo-esophageal fistula and multiple hemivertebrae.
This infant died of congestive failure on two days after birth. His right, forearm was flexed, abducted and shorter than the left, the thumb showed the characteristic feature of "finger like" deformity.
On X-ray films of spine and skeletal system, aplasia of the rt. radius and the occurence of multiple hemivertebrae. on thoracic and lumbar spines were proved. The cardiac shadow was globular and the pulmonary congestion was. seen on the chest film.
The autopsy findings showed -that the esophagus consisted of an upper segment which ended in a blind pouch above the level of the bifurcation of the trachea, the exact distant was 4 cm. from the gingiva, and a lower segment from the stomach which is connected to the bifurcation of the trachea by a short fistulous tract.
The aorta was coarctated at the off-spring of, the left clavicular artery, and the internal diameter was 0.6 cm. The diameter of pulmonary artery was 2.3cm. and the large ductus arteriosus (1.7cm. diameter) was entered to the below of coarctation from the near of right pulmonary artery bifurcation.

키워드

원문 및 링크아웃 정보

등재저널 정보