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Dental treatment for a patient with Edward’s syndrome under general anesthesia: Case report

대한장애인치과학회지 2020년 16권 1호 p.53 ~ 58
Ryu Gi-Youn, 송지수, 신터전, 현홍근, 김정욱, 장기택, 이상훈, 김영재,
소속 상세정보
 ( Ryu Gi-Youn ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
송지수 ( Song Ji-Soo ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
신터전 ( Shin Teo-Jeon ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
현홍근 ( Hyun Hong-Keun ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
김정욱 ( Kim Jung-Wook ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
장기택 ( Jang Ki-Taeg ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
이상훈 ( Lee Sang-Hoon ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
김영재 ( Kim Young-Jae ) - Seoul National University School of Dentistry Department of Pediatric Dentistry

Abstract


Edward’s syndrome (ES, trisomy 18) is a congenital chromosomal disorder that presents with an extra chromosome 18. The most common characteristics of this disorder are mental and growth retardation, congenital heart disease, craniofacial features (such as a prominent occiput, microcephaly, micrognathia, and low-set and malformed ears), clenched fists with overlapping fingers, finger flexion, and rocker-bottom feet. The dental characteristic of ES includes cleft lip/palate, high and narrow palate, anterior open bite, and vertical facial growth. Herein, we have described the dental treatment provided to a 4-year-old girl with ES.
The patient had visited the Seoul National University Dental Hospital with multiple caries in the primary teeth. The provision of dental care for patients with ES is generally complicated owing to factors such as poor cooperation, congenital cardiac abnormalities, and difficulty in maintaining the airway due to the presence of facial malformations. In this study, dental treatment was successfully performed under general anesthesia. Dental professionals need to be familiar with the clinical features of ES and provide continuous preventive therapies for these patients.

키워드

Edward’s syndrome; Trisomy 18; Mosaic trisomy; Dental treatment; General anesthesia

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